Background
Quantitative ultrasound (QUS) evaluates bone structural integrity by measuring changes in speed and attenuation of sound waves. These parameters are combined to form indices that predict bone fractures independent of BMD and FRAX. Indices include a “stiffness index’’ (SI) for Lunar devices, and a “quantitative ultrasound index” (QUI) for Hologic systems. SI and QUI are heritable, yet the underlying genetic determinants remain uncharacterised.
Purpose
To quantify the genetic similarity of SI and QUI, identify shared genetic determinants, and evaluate their relationship with fractures.
Methods
Genome-wide association studies (GWAS) were conducted on standardised measures of QUI in the UK-Biobank (N=447,873) and SI in the Taiwan Biobank (N=96,991). Pairwise genetic correlations correcting for genetic ancestry were estimated. QUI and SI GWAS were meta-analysed using a random effects method and clumped with ancestry-matched data. Associated variants were followed-up in GWAS of hip and forearm fractures. The closest protein coding gene to each associated variant was followed up in a single-cell transcriptomics dataset of murine bone and marrow cells, and the MGI mutant mouse database.
Results
QUI and SI were highly genetically correlated rg=0.83(CI95:0.73–0.92). 1,637 associated variants were identified (pmeta<5×10-8). 31 were robustly associated with forearm fractures (p<5×10-8), but not with hip fractures (p>0.05, Figure.1). 58 were located >1mb away from known DXA/QUS GWAS loci and deemed novel. Four novel variants were associated with forearm fractures [RYBP, CACNB2, IGF1 and HMGA1 (p<0.05)], and 2 with hip fractures (DRG1 and HMGA1). Genes closest to novel variants were differentially expressed in osteoblasts (e.g., CDH11), osteoclasts (S100A10), endothelial (FKBP1C) and vascular cells (CRIM1). CRIM1 resulted in abnormal skeletal phenotypes when mutated in mice.
Conclusions
Genetic determinants of QUI and SI are largely shared and highlight that such phenotypes enable the discovery of genes that may control bone structural integrity and fracture susceptibility.